NBME-style questions › Restrictive Lung Disease
Restrictive Lung Disease · NBME-Style

Restrictive Lung Disease — NBME-style practice question

A physician-validated, board-style question from the Active Transport QBank. Try it, then check the reasoning for every option.

A 31 year-old African-American female presents with a painful shin nodules, uveitis, and calcified hilar lymph nodes. A transbronchial biopsy of the lung would most likely show which of the following histologies?

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Answer: D. A young African-American woman with painful shin nodules (ERYTHEMA NODOSUM), uveitis, and bilateral hilar lymphadenopathy with calcification has SARCOIDOSIS. Transbronchial biopsy of the lung would show NON-CASEATING GRANULOMAS, the histologic hallmark. Sarcoidosis is a multisystem granulomatous disorder of unknown etiology with a striking demographic predilection for African-American women aged 20–40. Pulmonary involvement (≥90% of cases) produces bilateral hilar lymphadenopathy and parenchymal infiltrates. Other features include: - LÖFGREN SYNDROME: erythema nodosum + bilateral hilar adenopathy + arthralgia + fever (this patient's presentation) - Uveitis (anterior or posterior) - Skin: lupus pernio, plaques, papules - Cardiac: conduction defects, cardiomyopathy - CNS: cranial nerve palsies (especially CN VII), neuroendocrine dysfunction - HYPERCALCEMIA from 1α-hydroxylase activity in granulomas converting 25-OH-D to 1,25-(OH)2-D - Elevated ACE (in ~60% of patients) The pathology shows NON-CASEATING granulomas — well-formed collections of epithelioid macrophages and multinucleated giant cells WITHOUT central necrosis. Compare to TB (CASEATING granulomas, AFB-positive). Asteroid bodies and Schaumann bodies may be seen within giant cells. Treatment: many cases resolve spontaneously; symptomatic disease is treated with corticosteroids, with methotrexate or biologics for refractory cases. **Why each option:** **A.** Silicosis (silica particles with collagen) would be seen in occupationally exposed patients (miners, sandblasters), with eggshell calcification of hilar nodes — but presents differently with progressive dyspnea and isn't associated with erythema nodosum and uveitis in this demographic. **B.** Golden-brown fusiform rods describe ASBESTOS (ferruginous) bodies — seen in asbestos-related lung disease, which causes pleural plaques and mesothelioma. Not the picture here. **C.** Patchy interstitial lymphoid infiltrate describes hypersensitivity pneumonitis or interstitial pneumonia — not the granulomatous, sarcoidosis picture. **D.** Correct. Non-caseating granulomas are the histologic hallmark of sarcoidosis. The clinical picture (African-American woman with Löfgren syndrome: erythema nodosum + bilateral hilar adenopathy + uveitis) is classic.

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